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Pathways of ammonia detoxification to GLN in muscles associated with enhanced intake of your BCAA and α-KG (cataplerosis) and instructed outcomes of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Favourable result of BCAA on ammonia detoxification to GLN may be blunted by GLN degradation to ammonia in enterocytes and kidneys. Pheny